Tracheobronchomegaly is a very rare
congenital disorder of the
lung primarily characterized by an abnormal widening of the upper airways.[2] The abnormally widened
trachea and mainstem
bronchi are associated with recurrent lower respiratory tract infection and copious purulent
sputum production, eventually leading to
bronchiectasis and other respiratory complications.[3]
Diagnosis
Woodring et al. (1991) suggested the following diagnostic criteria for tracheomegaly in adults based on chest radiography:[4]
Adult Males: Tracheal transverse diameter > 25 mm and sagittal diameter > 27 mm.
Adult Females: Tracheal transverse diameter > 21 mm and sagittal diameter > 23 mm.
History
The term "Mounier-Kuhn syndrome" derives from the characterization of the condition by Prof. Pierre-Louis Mounier-Kuhn in 1932, while the name "tracheobronchomegaly" was introduced by Katz et al. in 1962.[5][6][7]
^Menon B, Aggarwal B, Iqbal A (2008). "Mounier-Kuhn syndrome: report of 8 cases of tracheobronchomegaly with associated complications". South Med J. 101 (1): 83–87.
doi:
10.1097/SMJ.0b013e31815d4259.
PMID18176298.
^KATZ I, LEVINE M, HERMAN P (December 1962). "Tracheobronchiomegaly. The Mounier-Kuhn syndrome". Am J Roentgenol Radium Ther Nucl Med. 88: 1084–94.
PMID13958486.
^Mounier-Kuhn P. Dilatation de la trachée: constatations radiographiques etbronchoscopiques. Lyon Med. 1932;150:106-9.